Unilateral Ovarian Dermoid Cyst Accompanied by an Ipsilateral Paratubal Cyst in a Girl with Proteus Syndrome Discovered by Laparoscopic Surgery
published online 15 October 2009.
Abstract
Background
Proteus syndrome is a rare hamartomatous disorder characterized by the overgrowth of multiple tissues in a mosaic pattern. Tumors of genitourinary tract in Proteus syndrome are uncommon.
Case
We here report a 5-year-old girl with Proteus syndrome who developed a cystic mass in the pelvic cavity. The cyst was discovered by ultrasonographic examination and finally proved to be a unilateral ovarian dermoid cyst accompanied by an ipsilateral paratubal cyst by laparoscopic surgery.
Summary and Conclusion
Proteus syndrome accompanied by an ovarian cyst is rare in girls. The possibilities of underlying ovarian cyst required for surgical intervention should be considered in Proteus syndrome.
1Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
2Department of Pathology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
Address correspondence to: Jae Kwan Lee, MD, Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, 80 Guro-gu Guro-dong, Seoul, 152-703, Korea.
ABSTRACT