Journal of Pediatric and Adolescent Gynecology
Volume 23, Issue 3 , Pages e107-e110, June 2010

Unilateral Ovarian Dermoid Cyst Accompanied by an Ipsilateral Paratubal Cyst in a Girl with Proteus Syndrome Discovered by Laparoscopic Surgery

  • Jin Hwa Hong, MD

      Affiliations

    • Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
  • ,
  • Jae Kwan Lee, MD

      Affiliations

    • Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
    • Corresponding Author InformationAddress correspondence to: Jae Kwan Lee, MD, Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, 80 Guro-gu Guro-dong, Seoul, 152-703, Korea.
  • ,
  • Seung Hun Song, MD

      Affiliations

    • Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
  • ,
  • Jong Ha Hwang, MD

      Affiliations

    • Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
  • ,
  • Kyung A. So, MD

      Affiliations

    • Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
  • ,
  • Bong Kyung Shin, MD

      Affiliations

    • Department of Pathology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
  • ,
  • Nak Woo Lee, MD

      Affiliations

    • Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea
  • ,
  • Kyu Wan Lee, MD

      Affiliations

    • Department of Obstetrics and Gynecology, Guro Hospital, College of Medicine, Korea University, Seoul, Korea

published online 15 October 2009.

Abstract 

Background

Proteus syndrome is a rare hamartomatous disorder characterized by the overgrowth of multiple tissues in a mosaic pattern. Tumors of genitourinary tract in Proteus syndrome are uncommon.

Case

We here report a 5-year-old girl with Proteus syndrome who developed a cystic mass in the pelvic cavity. The cyst was discovered by ultrasonographic examination and finally proved to be a unilateral ovarian dermoid cyst accompanied by an ipsilateral paratubal cyst by laparoscopic surgery.

Summary and Conclusion

Proteus syndrome accompanied by an ovarian cyst is rare in girls. The possibilities of underlying ovarian cyst required for surgical intervention should be considered in Proteus syndrome.

Key Words: Proteus syndrome, Dermoid cyst, Paratubal cyst, Laparoscopic surgery

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PII: S1083-3188(09)00295-2

doi:10.1016/j.jpag.2009.08.010

Journal of Pediatric and Adolescent Gynecology
Volume 23, Issue 3 , Pages e107-e110, June 2010