Sex Cord Tumor with Annular Tubules in a Young Adolescent with Von Willebrand's Disease
published online 06 November 2009.
Abstract
Background
Ovarian sex cord tumor with annular tubules (SCTAT) is a rare form of ovarian neoplasm.
Case
A 12-year-old female presented with menometrorrhagia. During her evaluation, she was both diagnosed with von Willebrand disease (VWD) and found to have an ovarian neoplasm, which was ultimately determined to be an ovarian sex cord tumor with annular tubules (SCTAT).
Summary and Conclusion
As her diagnosis was temporally associated with her worsening symptoms and the presence of an ovarian mass, this tumor may have played a role in her VWD diagnosis. There are no previously reported cases of SCTAT associated with VWD. This case reminds physicians of the importance of evaluating patients with menometrorrhagia for bleeding conditions, in addition to considering hormone-secreting ovarian neoplasms, including SCTAT.
1Department of Obstetrics and Gynecology, Baylor College of Medicine, Houston, Texas
2Department of Pathology, Baylor College of Medicine, Houston, Texas
Address correspondence to: Jennifer L. Bercaw, MD, 6620 Main St, Suite 1450, Houston, TX 77030; Phone: (713) 798-5052; Fax: (713) 798-7957.
ABSTRACT