Abstract
The association of obstructed hemivagina with ipisilateral renal anomaly (OHVIRA)
is a well-described entity. While there has been an increased familiarity with this
disorder, the exact incidence of OHVIRA is unknown. Our aim was to review the available
literature on this topic, look at common presentations, and uncommon presentations.
This condition is a well-described entity but requires careful evaluation, because
unique presentations do occur. Diagnostic challenges include time of presentation
and symptoms associated with presentation. Surgical challenges include microperforation
of the hemivaginal septum, pelvic inflammatory disease, thick septum, or high septum.
Each of these must be managed carefully. Although a solitary kidney is frequently
thought to be associated with OHVIRA, dysplastic kidneys, pelvic kidneys, or ectopic
ureters can occur. Prompt and accurate diagnosis is essential for relief of symptoms
and prevention of complications. To minimize problems associated with delayed diagnosis,
magnetic resonance imaging evaluation is recommended along with referral to a center
with expertise in these conditions.
Key Words
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Article info
Publication history
Published online: September 25, 2014
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© 2016 North American Society for Pediatric and Adolescent Gynecology. Published by Elsevier Inc. All rights reserved.
