Case Report| Volume 30, ISSUE 3, P425-428, June 2017

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Assembling a Functional Clitoris and Vulva from a Pseudo-Penis: A Surgical Technique for an Adult Woman with Congenital Adrenal Hyperplasia

  • Wiebren A.A. Tjalma
    Address correspondence to: Wiebren A.A. Tjalma, MD, PhD, Multidisciplinary Breast Clinic, Gynecological Oncology Unit, Department of Obstetrics and Gynecology, Wilrijkstraat 10, 2650 Edegem, Belgium; Phone: +32 3-821-5904
    Multidisciplinary Breast Clinic, Gynecological Oncology Unit and the Department of Obstetrics and Gynecology, Antwerp University Hospital, University of Antwerp, Edegem, Belgium
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Published:December 12, 2016DOI:



      Congenital adrenal hyperplasia (CAH) is associated with a genital deformation that might cause a negative body image. The genital ambiguity is generally “corrected” surgically during early infancy. The advantage is a psychological benefit. The disadvantages are multiple surgical procedures and the loss of orgasm.


      A 22-year-old woman with CAH consulted for genital reconstructive surgery. She had a pseudopenis of 4 cm and could achieve an orgasm by masturbating. During surgery, the penis was dismantled and with the preserved glans penis and the corpora cavernosa, a clitoris and vestibules were constructed, respectively. On the basis of the anamneses during the follow-up, she had a functional vagina and could still achieve orgasms.

      Summary and Conclusion

      Genital correction surgery for CAH at an older age was easier, could be done in 1 step, and enabled the preservation of orgasm.

      Key Words

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