Abstract
Background
Granular cell tumors (GCTs) are rare soft tissue lesions that can involve the female
genital tract, including the vulva. Although malignant tumors are aggressive and uncommon,
benign and atypical lesions still have associated risks, including recurrence and
multisite development.
Cases
Four cases of pediatric vulvar GCT are presented, including 1 atypical and 3 benign
tumors. The atypical lesion occurred in a 3-year-old girl, to our knowledge, the youngest
reported patient with GCT of the vulva. Follow-up information is available for 3 patients,
ranging 0-12 years.
Summary and Conclusion
GCTs are an important differential diagnosis in patients with vulvar lesions. In the
pediatric population, the tumors' risk of recurrence and multisite development require
gynecologists to advocate for complete resection, careful follow-up, and thorough
examination for additional tumor sites.
Key Words
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Article info
Publication history
Published online: January 03, 2018
Footnotes
The authors indicate no conflicts of interest.
Identification
Copyright
© 2018 North American Society for Pediatric and Adolescent Gynecology. Published by Elsevier Inc.
