Background
Abdominal fibromatosis presenting as an abdominal mass is a rare occurrence in a gynecological
setting. The diagnosis might not be suspected preoperatively, and management could
be challenging.
Case
An 18-year-old girl with ovarian germ cell malignancy was managed with staging laparotomy
and chemotherapy. She developed a large abdominal mass 10 months later. An abdominopelvic
mass (40 × 20 cm) was removed at laparotomy. The histopathological diagnosis was intra-abdominal
fibromatosis. A rapidly growing abdominal mass recurred postoperatively. After discussion
with the tumor board, chemotherapy with methotrexate and vinblastine was started.
The tumor was not responsive, and the patient succumbed after the second cycle of
chemotherapy.
Summary and Conclusion
Abdominal fibromatosis should be considered among the differential diagnoses of a
rapidly growing abdominal mass after resection of an ovarian germ cell tumor.
Key Words
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Article info
Publication history
Published online: December 23, 2021
Accepted:
December 16,
2021
Received in revised form:
November 25,
2021
Received:
September 14,
2021
Identification
Copyright
© 2021 North American Society for Pediatric and Adolescent Gynecology. Published by Elsevier Inc. All rights reserved.
